General Information of Disease (ID: DIS29QHF)

Disease Name Testicular sex cord-stromal neoplasm
Synonyms
sex cord-stromal tumour of the testis; sex cord-stromal tumor of the testis; sex cord-stromal neoplasm of the testis; sex cord-stromal neoplasm of testis; sex cord-stromal neoplasm; testis sex cord-stromal tumour; testis sex cord-stromal tumor; testicular sex cord-stromal tumour; testicular sex cord-stromal tumor; testicular sex cord-stromal neoplasm; sex cord-stromal tumour of testis; sex cord-stromal tumor of testis
Definition
A benign or malignant tumor that arises from the testis. It is composed of granulosa cells, Leydig cells, Sertoli cells, and fibroblasts. Each of these cell types may constitute the only cellular component that is present in the tumor or it may be mixed with other cell types in various combinations. The prognosis can not always be predicted on histologic grounds alone. Approximately, ten percent of these tumors may metastasize. Representative examples include granulosa cell tumor, Leydig cell tumor, Sertoli cell tumor, and tumors of the thecoma-fibroma group.
Disease Hierarchy
:
DISK4XHT: Neoplasm of testis
DIS29QHF: Testicular sex cord-stromal neoplasm
Disease Identifiers
MONDO ID
MONDO_0003125
UMLS CUI
C3840076
MedGen ID
825921
Orphanet ID
363489
SNOMED CT ID
702406000