Details of Disease
General Information of Disease (ID: DISCIZYS)
| Disease Name | Peeling skin syndrome | ||||
|---|---|---|---|---|---|
| Synonyms |
familial continuous skin peeling; skin peeling syndrome; idiopathic deciduous skin; peeling skin disease; familial continuous skin peeling syndrome; deciduous skin; PSS; keratosis exfoliativa congenita
|
||||
| Definition |
Peeling skin syndrome (PSS) refers to a group of rare autosomal recessive forms of ichthyosis that is characterized clinically by superficial, asymptomatic, spontaneous peeling of the skin and histologically by a shedding of the outer layers of the epidermis. PSS presents with either an acral (acral PSS) or a generalized distribution (generalized PSS type A (non inflammatory) or B (inflammatory)). Some cases remain difficult to classify, suggesting that there could be additional subtypes of PSS.
|
||||
| Disease Hierarchy | |||||