General Information of Disease (ID: DISEECV2)

Disease Name Functional pancreatic neuroendocrine tumor
Synonyms
functioning neuroendocrine tumour of pancreas; functioning neuroendocrine tumor of pancreas; functioning well-differentiated pancreatic neuroendocrine neoplasm; functional pancreatic neuroendocrine tumor; functioning PNET; syndromic pancreatic neuroendocrine tumor; functioning pancreatic endocrine tumor; functioning well-differentiated pancreatic NEN; syndromic pancreatic NET; functioning well differentiated pancreatic endocrine neoplasm; functioning pancreatic NET; functioning pancreatic neuroendocrine tumour; syndromic pancreatic neuroendocrine tumour; functioning well differentiated pancreatic endocrine tumor; functioning well differentiated pancreatic endocrine tumour; functional pancreatic NET; functioning well-differentiated neuroendocrine neoplasm of pancreas; functioning well-differentiated NEN of pancreas; functioning pancreatic endocrine tumour; functioning pancreatic neuroendocrine tumor
Definition
A low or intermediate grade well differentiated tumor with neuroendocrine differentiation that arises from the pancreas. It is characterized by the presence of a clinical syndrome that results from hormone hypersecretion.
Disease Hierarchy
DISDMPU0: Pancreatic neuroendocrine tumor
:
DISEECV2: Functional pancreatic neuroendocrine tumor
Disease Identifiers
MONDO ID
MONDO_0023206
UMLS CUI
C1708107
MedGen ID
310778
Orphanet ID
506060