General Information of Disease (ID: DISG6V5T)

Disease Name Dendritic cell tumor
Synonyms Dendritic cell neoplasm; Dendritic cell tumor, Not otherwise specified; Dendritic cell sarcoma, NOS; Dendritic cell tumor, NOS; Dendritic cell sarcoma, Not otherwise specified
Definition
A dendritic cell tumor develops from the cells of the immune system. This condition typically begins in the lymph system and may spread to nearby organs or distant parts of the body (metastasize). There are five subtypes of dendritic cell tumors: follicular dendritic cell tumor, interdigitating dendritic cell tumor, Langerhans' cell histiocytosis, Langerhans' cell sarcoma, and dendritic cell sarcoma not specified otherwise. The symptoms and severity of the condition depend on the subtype and location of the tumor. Treatment may include surgery, radiation therapy, and/or chemotherapy.
Disease Hierarchy
DISTBY9Z: Tumour
:
DISG6V5T: Dendritic cell tumor
Disease Identifiers
MONDO ID
MONDO_0020082
UMLS CUI
C5681852
MedGen ID
1842732
Orphanet ID
98289