General Information of Disease (ID: DISPJVH5)

Disease Name Benign PEComa
Synonyms
benign neoplasm with perivascular epithelioid cell differentiation; typical PEComa; neoplasm with perivascular epithelioid cell differentiation, benign; benign PEComa, nos; benign PEComa, not otherwise specified; benign PEComa
Definition A tumor with perivascular epithelioid cell differentiation characterized by the absence of pleomorphism and scarcity or absence of mitotic figures.
Disease Hierarchy
DIS8V0NT: Neoplasm with perivascular epithelioid cell differentiation
DISOHT1D: Benign soft tissue neoplasm
DISPJVH5: Benign PEComa
Disease Identifiers
MONDO ID
MONDO_0020581
UMLS CUI
C3839685
MedGen ID
825530
SNOMED CT ID
703604002