Details of Disease
General Information of Disease (ID: DISXD5AM)
| Disease Name | Autoimmune enteropathy | |||||
|---|---|---|---|---|---|---|
| Synonyms | immune-mediated protracted diarrhea of infancy; immune-mediated protracted diarrhoea of infancy; severe immune-mediated enteropathy | |||||
| Definition |
Severe-immune mediated enteropathy describes a variety of intestinal disorders that can range from a serious, early-onset systemic disease (IPEX) to a mild isolated gastrointestinal disease. In children it manifests with severe diarrhea and dehydration in the presence of characteristic antibodies (anti-enterocyte and anti-goblet cell) and in adults with chronic diarrhea, malabsorption and weight loss.
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