Details of Disease
General Information of Disease (ID: DIS3W5M5)
| Disease Name | Isolated agammaglobulinemia | |||||
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| Synonyms | isolated hypogammaglobulinemia; nonsyndromic agammaglobulinemia | |||||
| Definition |
Isolated agammaglobulinemia (IA) is the non-syndromic form of agammaglobulinemia, a primary immunodeficiency disease, and is characterized by deficient gamma globulins and associated predisposition to frequent and recurrent infections from infancy.
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