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Milrinone FDA Label
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ClinicalTrials.gov (NCT02319005) ENDEAVOUR: Phase 3 Multicenter Study of Revusiran (ALN-TTRSC) in Patients With Transthyretin (TTR) Mediated Familial Amyloidotic Cardiomyopathy (FAC). U.S. National Institutes of Health.
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Clinical pipeline report, company report or official report of the Pharmaceutical Research and Manufacturers of America (PhRMA)
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ADAMs family and relatives in cardiovascular physiology and pathology.J Mol Cell Cardiol. 2016 Apr;93:186-99. doi: 10.1016/j.yjmcc.2015.10.031. Epub 2015 Oct 29.
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An Alpha-1A Adrenergic Receptor Agonist Prevents Acute Doxorubicin Cardiomyopathy in Male Mice.PLoS One. 2017 Jan 12;12(1):e0168409. doi: 10.1371/journal.pone.0168409. eCollection 2017.
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Discovery of Genomic Characteristics and Selection Signatures in Korean Indigenous Goats Through Comparison of 10 Goat Breeds.Front Genet. 2019 Aug 8;10:699. doi: 10.3389/fgene.2019.00699. eCollection 2019.
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Role of complement C5a and histones in septic cardiomyopathy.Mol Immunol. 2018 Oct;102:32-41. doi: 10.1016/j.molimm.2018.06.006. Epub 2018 Jun 18.
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Dysfunction of dysferlin-deficient hearts.J Mol Med (Berl). 2007 Nov;85(11):1203-14. doi: 10.1007/s00109-007-0253-7. Epub 2007 Sep 9.
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Administration of Fenofibrate Markedly Elevates Fabp3 in Rat Liver and Plasma and Confounds Its Use as a Preclinical Biomarker of Cardiac and Muscle Toxicity.Lipids. 2018 Oct;53(10):947-960. doi: 10.1002/lipd.12110.
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Myocardial Fas ligand expression increases susceptibility to AZT-induced cardiomyopathy.Cardiovasc Toxicol. 2007;7(4):255-63. doi: 10.1007/s12012-007-9004-9. Epub 2007 Oct 18.
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Muscle death participates in myofibrillar abnormalities in FHL1 knockout mice.Biochem Biophys Res Commun. 2020 Feb 26;523(1):105-111. doi: 10.1016/j.bbrc.2019.12.026. Epub 2019 Dec 10.
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GADD45B inhibits MKK7-induced cardiac hypertrophy and the polymorphisms of GADD45B is associated with inter-ventricular septum hypertrophy.Biochem Biophys Res Commun. 2008 Aug 8;372(4):623-8. doi: 10.1016/j.bbrc.2008.05.122. Epub 2008 Jun 2.
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Disease Model of GATA4 Mutation Reveals Transcription Factor Cooperativity in Human Cardiogenesis.Cell. 2016 Dec 15;167(7):1734-1749.e22. doi: 10.1016/j.cell.2016.11.033.
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A GRK5 polymorphism that inhibits beta-adrenergic receptor signaling is protective in heart failure.Nat Med. 2008 May;14(5):510-7. doi: 10.1038/nm1750. Epub 2008 Apr 20.
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Glycogen Synthase Kinase-3 Promotes Fatty Acid Uptake and Lipotoxic Cardiomyopathy.Cell Metab. 2019 May 7;29(5):1119-1134.e12. doi: 10.1016/j.cmet.2019.01.005. Epub 2019 Feb 7.
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Inflammation leads through PGE/EP(3) signaling to HDAC5/MEF2-dependent transcription in cardiac myocytes.EMBO Mol Med. 2018 Jul;10(7):e8536. doi: 10.15252/emmm.201708536.
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Dysfunction of the CNS-heart axis in mouse models of Huntington's disease.PLoS Genet. 2014 Aug 7;10(8):e1004550. doi: 10.1371/journal.pgen.1004550. eCollection 2014 Aug.
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Patients with Dilated Cardiomyopathy and Sustained Monomorphic Ventricular Tachycardia Show Up-Regulation of KCNN3 and KCNJ2 Genes and CACNG8-Linked Left Ventricular Dysfunction.PLoS One. 2015 Dec 28;10(12):e0145518. doi: 10.1371/journal.pone.0145518. eCollection 2015.
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Reduced myocyte complex N-glycosylation causes dilated cardiomyopathy.FASEB J. 2019 Jan;33(1):1248-1261. doi: 10.1096/fj.201801057R. Epub 2018 Aug 23.
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Cardiac-Specific Overexpression of Oxytocin Receptor Leads to Cardiomyopathy in Mice.J Card Fail. 2018 Jul;24(7):470-478. doi: 10.1016/j.cardfail.2018.05.004. Epub 2018 May 23.
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An abnormal gene expression of the beta-adrenergic system contributes to the pathogenesis of cardiomyopathy in cirrhotic rats.Hepatology. 2008 Dec;48(6):1913-23. doi: 10.1002/hep.22533.
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Endurance exercise resistance to lipotoxic cardiomyopathy is associated with cardiac NAD(+)/dSIR2/PGC-1 pathway activation in old Drosophila.Biol Open. 2019 Oct 17;8(10):bio044719. doi: 10.1242/bio.044719.
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Inhibition of PIKfyve prevents myocardial apoptosis and hypertrophy through activation of SIRT3 in obese mice.EMBO Mol Med. 2017 Jun;9(6):770-785. doi: 10.15252/emmm.201607096.
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Impaired NF-B signalling underlies cyclophilin D-mediated mitochondrial permeability transition pore opening in doxorubicin cardiomyopathy.Cardiovasc Res. 2020 May 1;116(6):1161-1174. doi: 10.1093/cvr/cvz240.
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New insights in the field of muscle glycogenoses.Curr Opin Neurol. 2013 Oct;26(5):544-53. doi: 10.1097/WCO.0b013e328364dbdc.
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G-protein inactivator RGS6 mediates myocardial cell apoptosis and cardiomyopathy caused by doxorubicin.Cancer Res. 2013 Mar 15;73(6):1662-7. doi: 10.1158/0008-5472.CAN-12-3453. Epub 2013 Jan 21.
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Hepatocyte-Specific SR-BI Gene Transfer Corrects Cardiac Dysfunction in Scarb1-Deficient Mice and Improves Pressure Overload-Induced Cardiomyopathy.Arterioscler Thromb Vasc Biol. 2018 Sep;38(9):2028-2040. doi: 10.1161/ATVBAHA.118.310946.
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A recessive homozygous p.Asp92Gly SDHD mutation causes prenatal cardiomyopathy and a severe mitochondrial complex II deficiency.Hum Genet. 2015 Aug;134(8):869-79. doi: 10.1007/s00439-015-1568-z. Epub 2015 May 26.
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Induction of SENP1 in myocardium contributes to abnormities of mitochondria and cardiomyopathy.J Mol Cell Cardiol. 2015 Feb;79:115-22. doi: 10.1016/j.yjmcc.2014.11.014. Epub 2014 Nov 21.
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Disruption of the dystrophin-glycoprotein complex in the cardiomyopathic hamster.J Biol Chem. 1993 Jun 5;268(16):11496-9.
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Impact of Compound Hypertonic Saline Solution on Decompensated Heart Failure.Int Heart J. 2017 Aug 3;58(4):601-607. doi: 10.1536/ihj.16-313. Epub 2017 Jul 13.
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Inflammation, oxidative stress, and glial cell activation characterize stellate ganglia from humans with electrical storm.JCI Insight. 2017 Sep 21;2(18):e94715. doi: 10.1172/jci.insight.94715. eCollection 2017 Sep 21.
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SGLT1 inhibition boon or bane for diabetes-associated cardiomyopathy.Fundam Clin Pharmacol. 2020 Apr;34(2):173-188. doi: 10.1111/fcp.12516. Epub 2019 Nov 19.
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EGFR tyrosine kinase inhibition decreases cardiac remodeling and SERCA2a/NCX1 depletion in streptozotocin induced cardiomyopathy in C57/BL6 mice.Life Sci. 2018 Oct 1;210:29-39. doi: 10.1016/j.lfs.2018.08.018. Epub 2018 Aug 11.
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Genome wide association study (GWAS) of Chagas cardiomyopathy in Trypanosoma cruzi seropositive subjects.PLoS One. 2013 Nov 20;8(11):e79629. doi: 10.1371/journal.pone.0079629. eCollection 2013.
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Classification of Genes: Standardized Clinical Validity Assessment of Gene-Disease Associations Aids Diagnostic Exome Analysis and Reclassifications. Hum Mutat. 2017 May;38(5):600-608. doi: 10.1002/humu.23183. Epub 2017 Feb 13.
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Stk38 Modulates Rbm24 Protein Stability to Regulate Sarcomere Assembly in Cardiomyocytes.Sci Rep. 2017 Mar 21;7:44870. doi: 10.1038/srep44870.
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TWEAK/Fn14 mediates atrial-derived HL-1 myocytes hypertrophy via JAK2/STAT3 signalling pathway.J Cell Mol Med. 2018 Sep;22(9):4344-4353. doi: 10.1111/jcmm.13724. Epub 2018 Jul 4.
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TRPC3-Nox2 complex mediates doxorubicin-induced myocardial atrophy.JCI Insight. 2017 Aug 3;2(15):e93358. doi: 10.1172/jci.insight.93358. eCollection 2017 Aug 3.
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Functional characterization of TRPM4 variants identified in sudden unexpected natural death.Forensic Sci Int. 2018 Dec;293:37-46. doi: 10.1016/j.forsciint.2018.10.006. Epub 2018 Oct 24.
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Integration of microarray profiles associated with cardiomyopathy and the potential role of Ube3a in apoptosis.Mol Med Rep. 2014 Feb;9(2):621-5. doi: 10.3892/mmr.2013.1848. Epub 2013 Dec 9.
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Disruption of valosin-containing protein activity causes cardiomyopathy and reveals pleiotropic functions in cardiac homeostasis.J Biol Chem. 2019 May 31;294(22):8918-8929. doi: 10.1074/jbc.RA119.007585. Epub 2019 Apr 21.
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Arrhythmogenic cardiomyopathy in a patient with a rare loss-of-function KCNQ1 mutation.J Am Heart Assoc. 2015 Jan 23;4(1):e001526. doi: 10.1161/JAHA.114.001526.
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ERK1/2 Phosphorylation of FHOD Connects Signaling and Nuclear Positioning Alternations in Cardiac Laminopathy.Dev Cell. 2019 Dec 2;51(5):602-616.e12. doi: 10.1016/j.devcel.2019.10.023.
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Mechanism of Cardiac Troponin C Calcium Sensitivity Modulation by Small Molecules Illuminated by Umbrella Sampling Simulations.J Chem Inf Model. 2019 Jun 24;59(6):2964-2972. doi: 10.1021/acs.jcim.9b00256. Epub 2019 May 29.
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Loss of VEGFB and its signaling in the diabetic heart is associated with increased cell death signaling.Am J Physiol Heart Circ Physiol. 2017 Jun 1;312(6):H1163-H1175. doi: 10.1152/ajpheart.00659.2016. Epub 2017 Mar 17.
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Cardiomyocyte-specific loss of mitochondrial p32/C1qbp causes cardiomyopathy and activates stress responses. Cardiovasc Res. 2017 Aug 1;113(10):1173-1185. doi: 10.1093/cvr/cvx095.
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Cardiomyopathy in murine models of systemic sclerosis.Arthritis Rheumatol. 2015 Feb;67(2):508-16. doi: 10.1002/art.38942.
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Cytokines in HIV-associated cardiomyopathy.Int J Cardiol. 2007 Aug 21;120(2):150-7. doi: 10.1016/j.ijcard.2006.11.143. Epub 2007 Mar 2.
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Combined deficiency of dystrophin and beta1 integrin in the cardiac myocyte causes myocardial dysfunction, fibrosis and calcification.Circ Res. 2008 May 9;102(9):1109-17. doi: 10.1161/CIRCRESAHA.108.173153. Epub 2008 Mar 13.
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Ceramide is a cardiotoxin in lipotoxic cardiomyopathy.J Lipid Res. 2008 Oct;49(10):2101-12. doi: 10.1194/jlr.M800147-JLR200. Epub 2008 May 30.
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Melatonin attenuates ER stress and mitochondrial damage in septic cardiomyopathy: A new mechanism involving BAP31 upregulation and MAPK-ERK pathway.J Cell Physiol. 2020 Mar;235(3):2847-2856. doi: 10.1002/jcp.29190. Epub 2019 Sep 18.
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ALU transposition induces familial hypertrophic cardiomyopathy.Mol Genet Genomic Med. 2020 Jan;8(1):e951. doi: 10.1002/mgg3.951. Epub 2019 Sep 30.
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Morphological and functional analyses of skeletal muscles from an immunodeficient animal model of limb-girdle muscular dystrophy type 2E.Muscle Nerve. 2018 Feb 24;58(1):133-44. doi: 10.1002/mus.26112. Online ahead of print.
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Phasic change and apoptosis regulation of JAK2/STAT3 pathway in a type 2 diabetic rat model.Am J Transl Res. 2019 Feb 15;11(2):911-930. eCollection 2019.
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Combinatorial genetic replenishments in myocardial and outflow tract tissues restore heart function in tnnt2 mutant zebrafish.Biol Open. 2019 Dec 9;8(12):bio046474. doi: 10.1242/bio.046474.
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Pancreatic cancer genomes reveal aberrations in axon guidance pathway genes.Nature. 2012 Nov 15;491(7424):399-405. doi: 10.1038/nature11547. Epub 2012 Oct 24.
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Functional and morphological abnormalities of mitochondria in human cells containing mitochondrial DNA with pathogenic point mutations in tRNA genes.J Biol Chem. 1994 Jul 22;269(29):19060-6.
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Angiotensin-converting enzyme 2 overexpression protects against doxorubicin-induced cardiomyopathy by multiple mechanisms in rats.Oncotarget. 2017 Apr 11;8(15):24548-24563. doi: 10.18632/oncotarget.15595.
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Interrelation between Expression of ADAM 10 and MMP 9 and Synthesis of Peroxynitrite in Doxorubicin Induced Cardiomyopathy.Biomol Ther (Seoul). 2013 Sep 30;21(5):371-80. doi: 10.4062/biomolther.2013.034.
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Type 5 adenylyl cyclase increases oxidative stress by transcriptional regulation of manganese superoxide dismutase via the SIRT1/FoxO3a pathway.Circulation. 2013 Apr 23;127(16):1692-701. doi: 10.1161/CIRCULATIONAHA.112.001212. Epub 2013 Mar 27.
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Cardioprotective effect of endogenous pituitary adenylate cyclase-activating polypeptide on Doxorubicin-induced cardiomyopathy in mice.Circ J. 2010 Jun;74(6):1183-90. doi: 10.1253/circj.cj-09-1024. Epub 2010 Apr 6.
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Effects of cardiac-restricted overexpression of the A(2A) adenosine receptor on adriamycin-induced cardiotoxicity.Am J Physiol Heart Circ Physiol. 2010 Jun;298(6):H1738-47. doi: 10.1152/ajpheart.00688.2009. Epub 2010 Apr 2.
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Doberman pinschers present autoimmunity associated with functional autoantibodies: A model to study the autoimmune background of human dilated cardiomyopathy.PLoS One. 2019 Jul 5;14(7):e0214263. doi: 10.1371/journal.pone.0214263. eCollection 2019.
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Disruption of type 5 adenylyl cyclase prevents -adrenergic receptor cardiomyopathy: a novel approach to -adrenergic receptor blockade.Am J Physiol Heart Circ Physiol. 2014 Nov 15;307(10):H1521-8. doi: 10.1152/ajpheart.00491.2014. Epub 2014 Sep 5.
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MRI Assessment of Cardiomyopathy Induced by 1-Adrenoreceptor Autoantibodies and Protection Through 3-Adrenoreceptor Overexpression.Sci Rep. 2017 Mar 9;7:43951. doi: 10.1038/srep43951.
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Lack of the mitochondrial protein acylglycerol kinase causes Sengers syndrome. Am J Hum Genet. 2012 Feb 10;90(2):314-20. doi: 10.1016/j.ajhg.2011.12.005. Epub 2012 Jan 26.
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Comparative evaluation of cannabinoid receptors, apelin and S100A6 protein in the heart of women of different age groups.BMC Cardiovasc Disord. 2018 Oct 4;18(1):190. doi: 10.1186/s12872-018-0923-0.
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The preventive effects of edible folic acid on cardiomyocyte apoptosis and survival in early onset triple-transgenic Alzheimer's disease model mice.Environ Toxicol. 2018 Jan;33(1):83-92. doi: 10.1002/tox.22498. Epub 2017 Oct 25.
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Indoxyl sulfate upregulates the cannabinoid type 1 receptor gene via an ATF3/c-Jun complex-mediated signaling pathway in the model of uremic cardiomyopathy.Int J Cardiol. 2018 Feb 1;252:128-135. doi: 10.1016/j.ijcard.2017.11.086. Epub 2017 Dec 2.
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Occurrence, mortality and predictors of complicated cardiac perforation in patients with CRT-D: Based on the National Inpatient Sample registry.Int J Cardiol. 2019 Oct 15;293:109-114. doi: 10.1016/j.ijcard.2019.05.018. Epub 2019 May 13.
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Interstitial fibrosis and microvascular disease of the heart in uremia: amelioration by a calcimimetic.Lab Invest. 2009 May;89(5):520-30. doi: 10.1038/labinvest.2009.7. Epub 2009 Feb 2.
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Anthracycline-related cardiomyopathy after childhood cancer: role of polymorphisms in carbonyl reductase genes--a report from the Children's Oncology Group.J Clin Oncol. 2012 May 1;30(13):1415-21. doi: 10.1200/JCO.2011.34.8987. Epub 2011 Nov 28.
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CCR5del32 genotype in human enteroviral cardiomyopathy leads to spontaneous virus clearance and improved outcome compared to wildtype CCR5.J Transl Med. 2018 Sep 4;16(1):249. doi: 10.1186/s12967-018-1610-8.
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Human complement receptor type 1 (CR1) protein levels and genetic variants in chronic Chagas Disease.Sci Rep. 2018 Jan 11;8(1):526. doi: 10.1038/s41598-017-18937-z.
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Time-dependent and tissue-specific accumulation of mtDNA and respiratory chain defects in chronic doxorubicin cardiomyopathy.Circulation. 2003 Nov 11;108(19):2423-9. doi: 10.1161/01.CIR.0000093196.59829.DF. Epub 2003 Oct 20.
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Left ventricular non-compaction associated with a genetic variant of the CYP2C9 gene.Heart Lung Circ. 2006 Aug;15(4):269-71. doi: 10.1016/j.hlc.2006.02.007. Epub 2006 Apr 3.
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The MEF2 transcriptional target DMPK induces loss of sarcomere structure and cardiomyopathy.Cardiovasc Res. 2018 Sep 1;114(11):1474-1486. doi: 10.1093/cvr/cvy091.
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Conditional cardiac overexpression of endothelin-1 induces inflammation and dilated cardiomyopathy in mice.Circulation. 2004 Jan 20;109(2):255-61. doi: 10.1161/01.CIR.0000105701.98663.D4. Epub 2004 Jan 12.
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Familial atrial fibrillation is a genetically heterogeneous disorder.J Am Coll Cardiol. 2003 Jun 18;41(12):2185-92. doi: 10.1016/s0735-1097(03)00465-0.
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Endogenous sulfur dioxide protects against isoproterenol-induced myocardial injury and increases myocardial antioxidant capacity in rats.Lab Invest. 2011 Jan;91(1):12-23. doi: 10.1038/labinvest.2010.156. Epub 2010 Aug 23.
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Phenotypic analysis of hemochromatosis subtypes reveals variations in severity of iron overload and clinical disease.Blood. 2018 Jul 5;132(1):101-110. doi: 10.1182/blood-2018-02-830562. Epub 2018 May 9.
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Rapidly progressive course of Trypanosoma cruzi infection in mice heterozygous for hexamethylene bis-acetamide inducible 1 (Hexim1) gene.Microbes Infect. 2018 Jan;20(1):25-36. doi: 10.1016/j.micinf.2017.09.001. Epub 2017 Sep 22.
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Treatment with an adenoviral vector encoding hepatocyte growth factor mitigates established cardiac dysfunction in doxorubicin-induced cardiomyopathy.Am J Physiol Heart Circ Physiol. 2008 Feb;294(2):H1048-57. doi: 10.1152/ajpheart.01102.2007. Epub 2007 Dec 14.
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Hsp10 and Hsp60 modulate Bcl-2 family and mitochondria apoptosis signaling induced by doxorubicin in cardiac muscle cells.J Mol Cell Cardiol. 2003 Sep;35(9):1135-43. doi: 10.1016/s0022-2828(03)00229-3.
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Open issues in Mucopolysaccharidosis type I-Hurler.Orphanet J Rare Dis. 2017 Jun 15;12(1):112. doi: 10.1186/s13023-017-0662-9.
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Interleukin 1 Receptor-Like 1 Protein (ST2) is a Potential Biomarker for Cardiomyopathy in Duchenne Muscular Dystrophy.Pediatr Cardiol. 2017 Dec;38(8):1606-1612. doi: 10.1007/s00246-017-1703-9. Epub 2017 Aug 18.
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Macrocyclic MEK1/2 inhibitor with efficacy in a mouse model of cardiomyopathy caused by lamin A/C gene mutation.Bioorg Med Chem. 2017 Feb 1;25(3):1004-1013. doi: 10.1016/j.bmc.2016.12.014. Epub 2016 Dec 9.
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Case Report: High Mannose-Binding Lectin Serum Determined by MBL2 Genotype and Risk for Clinical Progression to Chagasic Cardiomyopathy: A Case Report of Three Patients.Am J Trop Med Hyg. 2019 Jan;100(1):93-96. doi: 10.4269/ajtmh.17-0701.
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Clinical and genetic characteristics of patients with fatty acid oxidation disorders identified by newborn screening.BMC Pediatr. 2018 Mar 8;18(1):103. doi: 10.1186/s12887-018-1069-z.
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Two Drosophila myosin transducer mutants with distinct cardiomyopathies have divergent ADP and actin affinities.J Biol Chem. 2011 Aug 12;286(32):28435-43. doi: 10.1074/jbc.M111.258228. Epub 2011 Jun 16.
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Adopting High-Resolution Allele Frequencies Substantially Expedites Variant Interpretation in Genetic Diagnostic Laboratories.J Mol Diagn. 2019 Jul;21(4):602-611. doi: 10.1016/j.jmoldx.2019.02.009. Epub 2019 Apr 25.
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Loss of Function Mutations in NNT Are Associated With Left Ventricular Noncompaction.Circ Cardiovasc Genet. 2015 Aug;8(4):544-52. doi: 10.1161/CIRCGENETICS.115.001026. Epub 2015 May 29.
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Partial restoration of cardiac function with PDZ nNOS in aged mdx model of Duchenne cardiomyopathy.Hum Mol Genet. 2014 Jun 15;23(12):3189-99. doi: 10.1093/hmg/ddu029. Epub 2014 Jan 25.
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Stabilization of Early Duchenne Cardiomyopathy With Aldosterone Inhibition: Results of the Multicenter AIDMD Trial.J Am Heart Assoc. 2019 Oct;8(19):e013501. doi: 10.1161/JAHA.119.013501. Epub 2019 Sep 24.
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Deletion of LOX-1 Protects against Heart Failure Induced by Doxorubicin.PLoS One. 2016 May 19;11(5):e0154994. doi: 10.1371/journal.pone.0154994. eCollection 2016.
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PARP-1 inhibition protects the diabetic heart through activation of SIRT1-PGC-1 axis.Exp Cell Res. 2018 Dec 15;373(1-2):112-118. doi: 10.1016/j.yexcr.2018.10.003. Epub 2018 Oct 23.
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A Novel Role of Cyclic Nucleotide Phosphodiesterase 10A in Pathological Cardiac Remodeling and Dysfunction.Circulation. 2020 Jan 21;141(3):217-233. doi: 10.1161/CIRCULATIONAHA.119.042178. Epub 2019 Dec 5.
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